Al-Basar International Journal of Ophthalmology

CASE REPORT
Year
: 2019  |  Volume : 6  |  Issue : 1  |  Page : 16--19

Role of scleral tectonic graft in saving the vision of a child with apert syndrome


Dinah Saad Ahmad Ibrahim1, Mohanad Kamaleldin Mahmoud Ibrahim2 
1 University of Khartoum, Faculty of Medicine, Department of Ophthalmology; Consultant Ophthalmologist, Albasar International Foundation, Khartoum, Sudan
2 Chief Executive MD, Albasar International Foundation, Makkah Eye Hospital; Assistant Professor of Community Medicine, Ibn Sina University, Faculty of Medicine, Department of Community Medicine, Khartoum, Sudan

Correspondence Address:
Dr. Dinah Saad Ahmad Ibrahim
Albasar International Foundation, Makkah Eye Hospital, Department of Ophthalmology, University of Khartoum, Khartoum
Sudan

Apert syndrome (AP) is a rare form of acrocehpalosyndactyly with autosomal-dominant transmission. The most common ocular features of patients with AP include proptosis, shallow orbits, and hypertelorism; they can have exotropia and antimongoloid slant of the palpebral fissures. The aim of this report was to study the role of scleral tectonic patch graft (STPG) in managing the corneal exposure due to AP. This was the clinical case report of a 9-year-old girl with AP, presented with right eye corneal perforation. She was treated with homologous STPG instead of tectonic corneal graft with good improvement of her visual acuity (VA). The outcome of the patient VA after 1 year was the improvement of the vision in the affected eye from the hand movement to 6/12, which was considered very satisfactory to the child and her family. This case report revealed that tectonic scleral patch graft is a sight-saving procedure in condition where the scleral tissue is readily available rather than the corneal tissue that needs the presence of cornel banks.


How to cite this article:
Ibrahim DS, Ibrahim MK. Role of scleral tectonic graft in saving the vision of a child with apert syndrome.Albasar Int J Ophthalmol 2019;6:16-19


How to cite this URL:
Ibrahim DS, Ibrahim MK. Role of scleral tectonic graft in saving the vision of a child with apert syndrome. Albasar Int J Ophthalmol [serial online] 2019 [cited 2020 Sep 20 ];6:16-19
Available from: http://www.bijojournal.org/article.asp?issn=1858-6538;year=2019;volume=6;issue=1;spage=16;epage=19;aulast=Ibrahim;type=0